Madelung's Deformity: Difference between revisions
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== Diagnosis == | == Diagnosis == | ||
==== '''Key | ==== '''Key Features from X-Ray''' ==== | ||
* increased dorsal and radial convexity of the distal radius | * increased dorsal and radial convexity of the distal radius | ||
* increased volar and ulnar tilt of the distal radial articular surface | * increased volar and ulnar tilt of the distal radial articular surface | ||
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==== '''MRI''' ==== | ==== '''MRI''' ==== | ||
MRI is done | MRI is done on the patients who need the surgical release of Vickers’ ligament to prevent deformity progression.<ref name=":1" /> | ||
== Differential Diagnosis == | == Differential Diagnosis == |
Revision as of 20:54, 25 December 2020
Introduction[edit | edit source]
Madelung’s deformity is a condition of the wrist characterized by a shortened distal radius with volar–ulnar curvature and a dorsally prominent distal ulna.[1]
A Vickers’ ligament is the feature to differentiate Madelung’s deformity from Madelung-like deformities.[2]
Epidemiology[edit | edit source]
Predominantly adolescent females are affected by a ratio of 4:1. The deformity is bilateral most often.[3]
Clinical Features[edit | edit source]
- Initially asymptomatic, progressive clinical deformity
- Pain at wrist
- Loss of wrist extension
- Compromised forearm rotation
- “Bayonet” deformity- prominent distal ulna as a result of dorsal subluxation[4]
- Girls are more often affected than boys
- Presents between the ages of 6 and 13 years[5]
Pathogenesis[edit | edit source]
Premature growth plate arrest at the medial volar aspect of the distal radius causes Madelung deformity. Repetitive traumatic pressure may result in Madelung-like deformity. Mutation or absence of the short stature homeobox (SHOX) gene is thought to be the cause of congenital madelung deformity.
Congenital madelung deformity can occur as a part of Leri-Weill dyschondrosteosis (LWD) or Turner syndrome.[6]
Diagnosis[edit | edit source]
Key Features from X-Ray[edit | edit source]
- increased dorsal and radial convexity of the distal radius
- increased volar and ulnar tilt of the distal radial articular surface
- widened interosseous space
- relative dorsal position of the ulnar head
- pyramiding of the carpus[3]
MRI[edit | edit source]
MRI is done on the patients who need the surgical release of Vickers’ ligament to prevent deformity progression.[5]
Differential Diagnosis[edit | edit source]
- Turner syndrome
- Nail-patella syndrome
- Hereditary, multiple exostosis
- Ollier’s disease
- Achondroplasia
- Multiple epiphyseal dysplasias
- Mucopolysaccharidoses (Hurler and Morquio syndrome)[7]
Treatment[edit | edit source]
Conservative Management[edit | edit source]
Conservative management of Madelung’s deformity may be helpful for skeletally mature patients with following measures:
Surgical Management[edit | edit source]
References[edit | edit source]
- ↑ Dubey A, Fajardo M, Green S, Lee SK. Madelung’s deformity: a review. Journal of Hand Surgery (European Volume). 2010 Mar;35(3):174-81.
- ↑ Prasad N, Venkatesh M. Madelung Deformity of the Wrist: A Classic Presentation. International Journal of Contemporary Medicine Surgery and Radiology. 2020;5:C4-5
- ↑ 3.0 3.1 Thomson C, Hawkes D, Nixon M. Madelung’s Deformity: Diagnosis, Classification and Treatment. Journal of Orthoplastic Surgery. 2020 Apr 17;4(1):1-1.
- ↑ Babu S, Turner J, Seewoonarain S, Chougule S. Madelung's Deformity of the Wrist—Current Concepts and Future Directions. Journal of wrist surgery. 2019 Jun;8(03):176-9.
- ↑ 5.0 5.1 Knutsen EJ, Goldfarb CA. Madelung's deformity. Hand. 2014 Sep;9(3):289-91.
- ↑ Tranmer A, Laub Jr D. Madelung deformity. Eplasty. 2016;16.
- ↑ K. Subbarao. (2019). Madelung and pseudo Madelung deformities-Pictorial essay. Journal of Medical and Scientific Research. 2019;7:1-6
- ↑ Shahi P, Sudan A, Sehgal A, Meher D, Meena U. Madelung Deformity of the Wrist Managed Conservatively. Cureus. 2020 May;12(5).
- ↑ Bebing M, de Courtivron B, Pannier S, Journeau P, Fitoussi F, Morin C, Violas P. Madelung's deformity in children: Clinical and radiological results from a French national multicentre retrospective study. Orthopaedics & Traumatology: Surgery & Research. 2020 Nov 1;106(7):1339-43.