Revised Hammersmith Scale (RHS) for Spinal Muscular Atrophy: Difference between revisions
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== Objective == | == Objective == | ||
The Revised Hammersmith Scale (RHS) is specifically design outcome measure for people affected by Spinal Muscular Atrophy (SMA)<ref>[http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0172346 Ramsey] D, Scoto M, Mayhew A, Main M, Mazzone ES, Montes J, et al. (2017) Revised Hammersmith Scale for spinal muscular atrophy: A SMA specific clinical outcome assessment tool. PLoS ONE 12(2): e0172346. doi:10.1371/journal. pone.0172346</ref> . The Hammersmith Functional Motor Scale (HFMS), was the first outcome measure designed to capture physical abilities in patients with SMA type 2 and 3<ref>Main M, Kairon H, Mercuri E, Muntoni F. The Hammersmith Functional Motor Scale for Children with Spinal Muscular Atrophy: a Scale to Test Ability and Monitor Progress in Children with Limited Ambulation. European Journal of Paediatric Neurology. 2003;7(4):155–9. pmid:12865054</ref>. An expanded version of the scale was published to be used for patients who were ambulant and it was named the Hammersmith Functional Motor Scale Expanded (HFMSE)<ref>O'Hagen JM, Glanzman AM, McDermott MP, Ryan PA, Flickinger J, Quigley J, et al. An expanded version of the Hammersmith Functional Motor Scale for SMA II and III patients. Neuromuscular disorders: NMD. 2007;17(9–10):693–7. Epub 2007/07/31. pmid:17658255</ref>. In recent years specialist from all over the world who are working with patients with SMA collaborated together to develop a much better scale by using Rasch analysis. The new scale was called RHS and it provides more sensitive description of SMA phenotype and progression of disease. | The Revised Hammersmith Scale (RHS) is specifically design outcome measure for people affected by Spinal Muscular Atrophy (SMA)<ref>[http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0172346 Ramsey] D, Scoto M, Mayhew A, Main M, Mazzone ES, Montes J, et al. (2017) Revised Hammersmith Scale for spinal muscular atrophy: A SMA specific clinical outcome assessment tool. PLoS ONE 12(2): e0172346. doi:10.1371/journal. pone.0172346</ref> . The Hammersmith Functional Motor Scale (HFMS), was the first outcome measure designed to capture physical abilities in patients with SMA type 2 and 3<ref>Main M, Kairon H, Mercuri E, Muntoni F. The Hammersmith Functional Motor Scale for Children with Spinal Muscular Atrophy: a Scale to Test Ability and Monitor Progress in Children with Limited Ambulation. European Journal of Paediatric Neurology. 2003;7(4):155–9. pmid:12865054</ref>. An expanded version of the scale was published to be used for patients who were ambulant and it was named the Hammersmith Functional Motor Scale Expanded (HFMSE)<ref>O'Hagen JM, Glanzman AM, McDermott MP, Ryan PA, Flickinger J, Quigley J, et al. An expanded version of the Hammersmith Functional Motor Scale for SMA II and III patients. Neuromuscular disorders: NMD. 2007;17(9–10):693–7. Epub 2007/07/31. pmid:17658255</ref>. In recent years specialist from all over the world who are working with patients with SMA collaborated together to develop a much better scale by using Rasch analysis. The new scale was called RHS and it provides more sensitive description of SMA phenotype and progression of disease. | ||
Revision as of 15:48, 30 August 2018
Top Contributors - Evelin Milev, Jeremy Bryan, Kim Jackson, Amrita Patro, Nikhil Benhur Abburi and Lucinda hampton
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Objective[edit | edit source]
The Revised Hammersmith Scale (RHS) is specifically design outcome measure for people affected by Spinal Muscular Atrophy (SMA)[1] . The Hammersmith Functional Motor Scale (HFMS), was the first outcome measure designed to capture physical abilities in patients with SMA type 2 and 3[2]. An expanded version of the scale was published to be used for patients who were ambulant and it was named the Hammersmith Functional Motor Scale Expanded (HFMSE)[3]. In recent years specialist from all over the world who are working with patients with SMA collaborated together to develop a much better scale by using Rasch analysis. The new scale was called RHS and it provides more sensitive description of SMA phenotype and progression of disease.
Intended Population[edit | edit source]
The RHS was developed to evaluate the broad spectrum of motor functions in patients with SMA. It detects changes for very weak SMA type 2 to very strong SMA type 3. With some of the new pharmaceutical approaches which show great improvements in the weaker end of the spectrum, now there are even children with type 1 who show enough skills in order to pick up points on the scale.
Method of Use[edit | edit source]
The RHS is an ordinal scale which consist of 33 items with grades of 0,1 and 2. For individuals who can achieve the task without any compensation it is given a score of 2. For those who only attempt the movement or finish it with some form of compensation is scored 1 and 0 is given for patients unable to perform the item.
Evidence[edit | edit source]
Reliability[edit | edit source]
Validity[edit | edit source]
Responsiveness[edit | edit source]
Miscellaneous[edit | edit source]
Links[edit | edit source]
References[edit | edit source]
- ↑ Ramsey D, Scoto M, Mayhew A, Main M, Mazzone ES, Montes J, et al. (2017) Revised Hammersmith Scale for spinal muscular atrophy: A SMA specific clinical outcome assessment tool. PLoS ONE 12(2): e0172346. doi:10.1371/journal. pone.0172346
- ↑ Main M, Kairon H, Mercuri E, Muntoni F. The Hammersmith Functional Motor Scale for Children with Spinal Muscular Atrophy: a Scale to Test Ability and Monitor Progress in Children with Limited Ambulation. European Journal of Paediatric Neurology. 2003;7(4):155–9. pmid:12865054
- ↑ O'Hagen JM, Glanzman AM, McDermott MP, Ryan PA, Flickinger J, Quigley J, et al. An expanded version of the Hammersmith Functional Motor Scale for SMA II and III patients. Neuromuscular disorders: NMD. 2007;17(9–10):693–7. Epub 2007/07/31. pmid:17658255
