Dropped Head Syndrome associated with Motor Neurone Disease
Original Editor - Eugenie Lamprecht
Top Contributors - Eugenie Lamprecht and Kim Jackson
Introduction[edit | edit source]
Dropped head syndrome (DHS) is a rare condition characterized by severe weakness of neck extensors and may associate with weakness of shoulder girdle and proximal arm muscles. This occurs as a result of several neurological, neuromuscular, muscular, and other causes[1].
Neurological conditions that may lead to DHS include;[edit | edit source]
- amyotrophic lateral sclerosis (ALS),
- Parkinson disease
- multiple system atrophy,
- cervical dystonia,
- postpolio syndrome,
- cervical myelopathy,
- chronic inflammatory polyneuropathy (CIDP),
- neuromuscular causes include myasthenia gravis (MG),
- Lambert-Eaton myasthenia syndrome (LEMS),
- muscular causes include primary inflammatory such as polymyositis,
- Scleromyositis,
- isolated inflammatory axial myopathy,
- primary non-inflammatory conditions (nemaline myopathy, mitochondrial myopathy, and congenital myopathy)
- isolated neck extensor myopathy (INEM).[2]